A Case of Erdheim-Chester Disease in a Patient with Langerhans Cell Histiocytosis
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Keywords
Erdheim-Chester disease, Langerhans cell histiocytosis, mixed histiocytosis, histopathology, immunohistochemistry
Abstract
Erdheim-Chester Disease (ECD) is a rare non-Langerhans cell histiocytosis with widely variable presentations. Cutaneous findings typically consist of yellow-brown papules and plaques on the eyelids, neck, axillae, trunk, and/or groin. ECD can be diagnosed along with or subsequently to Langerhans Cell Histiocytosis (LCH), constituting a mixed histiocytosis phenotype. In this Brief Article, we present the case of a patient with LCH who developed new lesions on the scalp and axillae consistent with ECD. We emphasize the consideration of co-occurring ECD or other mixed phenotypes in patients diagnosed LCH who develop new cutaneous findings.
References
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